Fibrous Hamartoma of Infancy
Definition
- Triphasic soft tissue mass (fibrous, adipose, primitive mesenchymal) presenting in infants
Diagnostic Criteria
- Most cases under age 4
- Congenital to 19 years
- Superficial soft tissue lesion
- Rarely attached to muscle or fascia
- Poorly circumscribed
- Triphasic lesion
- Spindle cell fibrous trabeculae
- Variably cellular
- Disorganized mature fat
- Islands of immature mesenchymal cells
- Small round to spindled cells
- Cytologically bland
- Scant cytoplasm, small blue cell pattern
- May be myxoid
- Trabeculae of immature mesenchymal cells may occasionally infiltrate fat
- Spindle cell fibrous trabeculae
- Mitotic figures rare in all components
- Scattered lymphocytes may be present
- Overlying skin may show eccrine changes
- Hyperplasia
- Duct dilation
- Intralumenal papillae
- Squamous metaplasia of ducts
Robert V Rouse MD
Department of Pathology
Stanford University School of Medicine
Stanford CA 94305-5342
Original posting : November 20, 2007
Last Update: March 26, 2014