Palmar Fibromatosis
Definition
- A nodular, cytologically bland fibroproliferative process that involves the palmar aponeuroses
Alternate / Historical Names
-
Dupuytren contracture
Diagnostic Criteria
- Most often involves palm
- May rarely involve dorsum of hand or wrist
- Involves aponeurosis and rarely overlying dermis
- No infiltration of deeper tissues
- Grossly forms multiple nodules 1 cm or less
- Infrequently forms a single dominant nodule
- Cellularity ranges from low to high
- Older lesions are densely collagenous
- Bland spindle cells
- Nuclei small and dark to moderate sized and vesicular
- Scant cytoplasm
- Mitotic figures may be frequent but not atypical
- Small foci of perivascular hemorrhage and hemosiderin may be present
- Metaplastic cartilage and bone are seen rarely
- Necrosis very rare
Robert V Rouse MD
Department of Pathology
Stanford University School of Medicine
Stanford CA 94305-5342
Original posting: November 29, 2007